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29.09.2022 | Original Article

Changes in postoperative quality of life of pediatric total colonic aganglionosis patients: effect of pull-through technique

verfasst von: Go Miyano, Keiichi Morita, Koichi Tsuboi, Seitaro Kosaka, Toshiaki Takahashi, Susumu Yamada, Shunsuke Yamada, Takanori Ochi, Shogo Seo, Hiroyuki Koga, Tsubasa Takahashi, Koji Fukumoto, Naoto Urushihara, Tadashi Hatakeyama, Tadaharu Okazaki, Toshihiro Yanai, Geoffrey J. Lane, Atsuyuki Yamataka

Erschienen in: Pediatric Surgery International | Ausgabe 12/2022

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Abstract

Aim

To assess mid-/long-term quality of life (QOL) of total colonic aganglionosis (TCA) patients.

Methods

Modified pre-existing QOL assessment tools for general lifestyle (GL), bowel function (BF), and mental health (MH) were administered to postoperative TCA patients from five institutions, who were at least 7 years old to compare Duhamel (with pouch) and Swenson/Soave (without pouch) techniques between children (Ch 7–12 years old), teenagers (Tn 13–19), and adults (Ad 20 and over). For MH, caregivers were also interviewed, but separately. Maximum scores were 12 for GL/MH and 18 for BF.

Results

There were 32 subjects. GL and BF scores increased significantly from Ch (GL 4.8 ± 2.5, BF: 11.3 ± 4.6) to Tn (GL 7.8 ± 2.6, BF 16.2 ± 3.0); scores for MH did not change significantly. Mean caregiver MH scores were significantly lower than mean subject MH scores for all age groups (subject scores: 10.1, 10.7, 10.7 versus caregiver scores: 6.8, 7.8, 8.1 for Ch, Tn, Ad, respectively). PT technique/presence of a pouch did not influence the incidence of enterocolitis or QOL scores.

Conclusion

MH responses showed subjects felt better than caregivers believed. This discrepancy could cause conflict despite steadily improving GL/BF. QOL was unaffected by PT technique/presence of a pouch.

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Titel: Changes in postoperative quality of life of pediatric total colonic aganglionosis patients: effect of pull-through technique
verfasst von: Go Miyano
Keiichi Morita
Koichi Tsuboi
Seitaro Kosaka
Toshiaki Takahashi
Susumu Yamada
Shunsuke Yamada
Takanori Ochi
Shogo Seo
Hiroyuki Koga
Tsubasa Takahashi
Koji Fukumoto
Naoto Urushihara
Tadashi Hatakeyama
Tadaharu Okazaki
Toshihiro Yanai
Geoffrey J. Lane
Atsuyuki Yamataka
Publikationsdatum: 29.09.2022
Verlag: Springer Berlin Heidelberg
Erschienen in: Pediatric Surgery International / Ausgabe 12/2022
Print ISSN: 0179-0358
Elektronische ISSN: 1437-9813
DOI: https://doi.org/10.1007/s00383-022-05239-3

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Changes in postoperative quality of life of pediatric total colonic aganglionosis patients: effect of pull-through technique

Abstract